Anaplastic lymphoma kinase (ALK)-positive histiocytosis is an uncommon condition. recently considered a separate condition from other histiocytosis by WHO 5th edition. It can involve intracranial structures. This manuscript describes a case of ALK-positive histiocytosis of the cavernous sinus. https://parisnaturalfoodes.shop/product-category/konjac-spaghetti/